Maria de Fátima Vieira Ventura
AuthID: R-000-B2W
11
TITLE: Substrate specificity of human carnitine acetyltransferase: Implications for fatty acid and branched-chain amino acid metabolism Full Text
AUTHORS: Sara Violante; Lodewijk Ijlst; Jos Ruiter; Janet Koster; Henk van Lenthe; Marinus Duran; Isabel Tavares de Almeida ; Ronald J A Wanders; Sander M Houten; Fatima V Ventura;
PUBLISHED: 2013, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1832, ISSUE: 6
AUTHORS: Sara Violante; Lodewijk Ijlst; Jos Ruiter; Janet Koster; Henk van Lenthe; Marinus Duran; Isabel Tavares de Almeida ; Ronald J A Wanders; Sander M Houten; Fatima V Ventura;
PUBLISHED: 2013, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1832, ISSUE: 6
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TITLE: Carnitine palmitoyltransferase 2 and carnitine/acylcarnitine translocase are involved in the mitochondrial synthesis and export of acylcarnitines
AUTHORS: Sara Violante; Lodewijk IJlst; Heleen te Brinke; Isabel Tavares de Almeida ; Ronald J A Wanders; Fatima V Ventura; Sander M Houten;
PUBLISHED: 2013, SOURCE: FASEB JOURNAL, VOLUME: 27, ISSUE: 5
AUTHORS: Sara Violante; Lodewijk IJlst; Heleen te Brinke; Isabel Tavares de Almeida ; Ronald J A Wanders; Fatima V Ventura; Sander M Houten;
PUBLISHED: 2013, SOURCE: FASEB JOURNAL, VOLUME: 27, ISSUE: 5
13
TITLE: Peroxisomes contribute to the acylcarnitine production when the carnitine shuttle is deficient Full Text
AUTHORS: Sara Violante; Lodewijk Ijlst; Heleen te Brinke; Janet Koster; Isabel Tavares de Almeida ; Ronald J A Wanders; Fatima V Ventura; Sander M Houten;
PUBLISHED: 2013, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS, VOLUME: 1831, ISSUE: 9
AUTHORS: Sara Violante; Lodewijk Ijlst; Heleen te Brinke; Janet Koster; Isabel Tavares de Almeida ; Ronald J A Wanders; Fatima V Ventura; Sander M Houten;
PUBLISHED: 2013, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS, VOLUME: 1831, ISSUE: 9
14
TITLE: THE HUMAN MEDIUM-CHAIN ACYL-COA DEHYDROGENASE P.G377V PROTEIN: A NOVEL DISEASE-CAUSING MUTANT AFFECTING MITOCHONDRIAL FATTY ACID BETA-OXIDATION
AUTHORS: Ventura, FV; Lopes, F; Louro, F; Luz, A; Ramos, R; Rocha, H; Vilarinho, L; Gaspar, A; Leandro, P; Tavares de Almeida, IT;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
AUTHORS: Ventura, FV; Lopes, F; Louro, F; Luz, A; Ramos, R; Rocha, H; Vilarinho, L; Gaspar, A; Leandro, P; Tavares de Almeida, IT;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
INDEXED IN: 
WOS
WOS15
TITLE: Carnitine palmitoyltransferase 2: New insights on the substrate specificity and implications for acylcarnitine profiling Full Text
AUTHORS: Sara Violante; Lodewijk Ijlst; Henk van Lenthe; Isabel Tavares de Almeida ; Ronald J Wanders; Fatima V Ventura;
PUBLISHED: 2010, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1802, ISSUE: 9
AUTHORS: Sara Violante; Lodewijk Ijlst; Henk van Lenthe; Isabel Tavares de Almeida ; Ronald J Wanders; Fatima V Ventura;
PUBLISHED: 2010, SOURCE: BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, VOLUME: 1802, ISSUE: 9
16
TITLE: Inhibition of adenine nucleotide transport in rat liver mitochondria by long-chain acyl-coenzyme A beta-oxidation intermediates Full Text
AUTHORS: Fatima V Ventura; Isabel Tavares de Almeida; Ronald J A Wanders;
PUBLISHED: 2007, SOURCE: BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, VOLUME: 352, ISSUE: 4
AUTHORS: Fatima V Ventura; Isabel Tavares de Almeida; Ronald J A Wanders;
PUBLISHED: 2007, SOURCE: BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, VOLUME: 352, ISSUE: 4
17
TITLE: Differential inhibitory effect of long-chain acyl-CoA esters on succinate and glutamate transport into rat liver mitochondria and its possible implications for long-chain fatty acid oxidation defects Full Text
AUTHORS: Ventura, FV; Ruiter, J; Ijlst, L; de Almeida, IT; Wanders, RJA;
PUBLISHED: 2005, SOURCE: MOLECULAR GENETICS AND METABOLISM, VOLUME: 86, ISSUE: 3
AUTHORS: Ventura, FV; Ruiter, J; Ijlst, L; de Almeida, IT; Wanders, RJA;
PUBLISHED: 2005, SOURCE: MOLECULAR GENETICS AND METABOLISM, VOLUME: 86, ISSUE: 3
18
TITLE: Quantitative acylcarnitine profiling in fibroblasts using [U-C-13] palmitic acid: an improved tool for the diagnosis of fatty acid oxidation defects Full Text
AUTHORS: Ventura, FV; Costa, CG; Struys, EA; Ruiter, J; Allers, P; Ijlst, L; de Almeida, T; Duran, M; Jakobs, C; Wanders, RJA;
PUBLISHED: 1999, SOURCE: CLINICA CHIMICA ACTA, VOLUME: 281, ISSUE: 1-2
AUTHORS: Ventura, FV; Costa, CG; Struys, EA; Ruiter, J; Allers, P; Ijlst, L; de Almeida, T; Duran, M; Jakobs, C; Wanders, RJA;
PUBLISHED: 1999, SOURCE: CLINICA CHIMICA ACTA, VOLUME: 281, ISSUE: 1-2
19
TITLE: Lactic acidosis in long-chain fatty acid beta-oxidation disorders Full Text
AUTHORS: Ventura, FV; Ruiter, JPN; Ijlst, L; De Almeida, IT; Wanders, RJA;
PUBLISHED: 1998, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 21, ISSUE: 6
AUTHORS: Ventura, FV; Ruiter, JPN; Ijlst, L; De Almeida, IT; Wanders, RJA;
PUBLISHED: 1998, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 21, ISSUE: 6
20
TITLE: Carnitine palmitoyltransferase II specificity towards beta-oxidation intermediates - Evidence for a reverse carnitine cycle in mitochondria Full Text
AUTHORS: Ventura, FV; Ijlst, L; Ruiter, J; Ofman, R; Costa, CG; Jakobs, C; Duran, M; De Almeida, IT ; Bieber, LL; Wanders, RJA;
PUBLISHED: 1998, SOURCE: EUROPEAN JOURNAL OF BIOCHEMISTRY, VOLUME: 253, ISSUE: 3
AUTHORS: Ventura, FV; Ijlst, L; Ruiter, J; Ofman, R; Costa, CG; Jakobs, C; Duran, M; De Almeida, IT ; Bieber, LL; Wanders, RJA;
PUBLISHED: 1998, SOURCE: EUROPEAN JOURNAL OF BIOCHEMISTRY, VOLUME: 253, ISSUE: 3
