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TITLE: High molecular weight forms of human phenylalanine hydroxylase: the role of the ACT domain in the balance between a fully functional protein and the large inactive aggregates  Full Text
AUTHORS: Leandro, J; Amaro, MP; Lino, PR; Flatmark, T; Leandro, P;
PUBLISHED: 2013, SOURCE: 38th Congress of the Federation-of-European-Biochemical-Societies (FEBS) in FEBS JOURNAL, VOLUME: 280
INDEXED IN: WOS
22
TITLE: Self-association of the regulatory domain of human phenylalanine hydroxylase: contribution to the protein instability  Full Text
AUTHORS: Leandro, J; Saraste, J; Leandro, P; Flatmark, T;
PUBLISHED: 2012, SOURCE: 22nd IUBMB Congress/37th FEBS Congress in FEBS JOURNAL, VOLUME: 279
INDEXED IN: WOS
23
TITLE: PROTEIN ENGINEERING TO OBTAIN PHENYLALANINE HYDROXYLASE PROTEINS WITH HIGHER STABILITY
AUTHORS: Lino, PR; Lourenco, C; Leandro, J; Tavares de Almeida, IT; Almeida, AJ; Leandro, P;
PUBLISHED: 2011, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 34
INDEXED IN: WOS
25
TITLE: A Stochastic Dynamic Methodology (StDM) to simulate the effects of fire on vegetation and bird communities in Pinus pinaster stands  Full Text
AUTHORS: Pedro Silva Santos; Helena Valentim; Antonio Luis; Luis Queiros; Paulo Travassos; Joao Alexandre Cabral ;
PUBLISHED: 2010, SOURCE: ECOLOGICAL INDICATORS, VOLUME: 10, ISSUE: 2
INDEXED IN: Scopus WOS
26
TITLE: THE EFFECT OF LOW-MOLECULAR-WEIGHT COMPOUNDS ON THE IN VITRO POLYMERIZATION/FIBRIL FORMATION PROCESS OF MUTANT G46S-HPAH  Full Text
AUTHORS: Leandro, J; Simonsen, N; Tavares T de Almeida; Leandro, P; Flatmark, T;
PUBLISHED: 2009, SOURCE: 11th International Conference of Inborn Errors of Metabolism in MOLECULAR GENETICS AND METABOLISM, VOLUME: 98, ISSUE: 1-2
INDEXED IN: WOS
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TITLE: Assembly of hybrid heteroallelic mutant forms of human phenylalanine hydroxylase produced in a prokaryotic dual vector expression system  Full Text
AUTHORS: Almeida, R; Leandro, J; Cristo, I; Tavares I de Almeida; Leandro, P;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
INDEXED IN: WOS
28
TITLE: Studies on the interaction of mutant forms of human phenylalanine hydroxylase with molecular chaperones  Full Text
AUTHORS: Cristo, I; Almeida, R; Leandro, J; de Almeida Tavares; Leandro, P;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
INDEXED IN: WOS
29
TITLE: Interallelic complementation and phenylketonuria: Isolation of hybrid forms of human phenylalanine hydroxylase (HPAH)  Full Text
AUTHORS: Leandro, J; de Almeida I Tavares; Leandro, P; Flatmark, T;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
INDEXED IN: WOS
30
TITLE: Phenylketonuria as a protein misfolding disease: Mutant PG46S human phenylalanine hydroxylase has a propensity to self-associate and form amyloid fibrils  Full Text
AUTHORS: Leandro, J; Simonsen, N; Tavares I de Almeida; Leandro, P; Flatmark, T;
PUBLISHED: 2008, SOURCE: JOURNAL OF INHERITED METABOLIC DISEASE, VOLUME: 31
INDEXED IN: WOS
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